A young prince in Luxembourg dies from a rare genetic disease

Amir Luxembourg died on 22 genetic disease that spent his short life raising awareness.

Prince Frederick, the second cousin of the Luxembourg throne, at the age of fourteen, discovered that he had a boom in Jin in Bulge, who participates in the repetition and repair of DNA. He died on March 1 in Paris, his father, Prince Robert, He said in a statement Through Polg.

Estimates differ, but nearly one out of every 10,000 people They think they have Polg, or Polimiries Gama, disease, according to the United Mitochondria Foundation. that it Mitochondria disorderA group of cases that affect how mitochondria is produced in energy cells. Polg disease affects multiple organs and can lead to episodes and poor coordination, among other symptoms.

Prince Robert said: “One can compare it to a defective battery that is not fully recharged, in the event of continuous drain and loses strength in the end,” Prince Robert said.

Polg deficiency is a particularly brutal type of mitochondria, according to Sir Doug Turnbul, an honorary professor of neuroscience at Newcastle University and a member of the Polg Consulting Council. He said: “It is progressive,” attacking many different systems with the same conclusion. “

Prince Frederick was a founder and creative director of Polg. Its DNA has used its research, and the studies that started Make a short movie About the disease. Friedrich also designed a money collection line to search.

Friedrich was born in AIX-EN-PROVINCE, France, and grew up in Switzerland. His father said, he was a fan of the American TV program “The Office”, and watched the full series 10 times.

In his last days, Frederick in the hospital had another serious pneumonia and infection that he left unable to move, but he could still search for the window, Prince Robert said.

His father said: “Through the small window covered with the network, he saw the Eiffel Tower glowing with dance every hour of lights.” Friedrich asked his brother, Alexander, to take a picture of the sun.

Frederick was the second cousin of Prince Gyum, who would take over the throne of Luxembourg when he was his father, Grand Duke HenryIt retires in October. Friedrich and clouds participate in the grandparents of grandparents: Charlotte, Duchess of Grand Luxembourg, which prevailed from 1919 to 1964, and her husband, Prince Felix.

“When you are a child, you have all these dreams, all these aspirations,” Frederick said in the movie produced by his organization. “I am not sure that I understood all the consequences of Polg when I was diagnosed first time. It is more accurate, as the world becomes smaller and smaller.”